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Suprasellar Primary Malignant Rhabdoid Tumor in an Adult : a case report Atsushi KUGE 1 , Takamasa KAYAMA 1 , Daisuke TSUCHIYA 1 , Keita KAWAKAMI 1 , Shinjiro SAITO 1 , Youichi NAKAZATO 2 , Hiroyoshi SUZUKI 3 1Department of Neurosurgery, Yamagata University School of Medicine Keyword: adult , malignant rhabdoid tumor , suprasellar lesion pp.351-358
Published Date 2000/4/10
DOI https://doi.org/10.11477/mf.1436901874
  • Abstract
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Malignant rhabdoid tumor (MRT), described for the first time in 1978 in the kidney, has rarely been re-ported in other organs including the brain and has involved adults in only 3 cases.

We described a case of MET in a 32-year-old woman who presented with severe headache, nausea and sudden onset of visual disturbance. MRI showed a well-enhanced mass at the suprasellar region. Subtotal removal of the tumor was performed. However, tumor regrowth occurred after the operation (doubling time, 8.36 days) and spinal dissemination was detected. Therefore, chemotherapy and radiotherapy were administered focusing on the suprasellar lesion and the spinal cord.

Pathologically, light micrographs showed rhabdoid cells with large, round, single or double nuclei with one prominent nucleolus and eosinophilic cytoplasmic inclusions. Electron micrographs were made of typic-al rhabdoid cells displaying bundles of intermediate filaments within the perikaryon. In immunohistoche-mical studies, EMA, vimentin, cytokeratin and SMA were positive. Pathological findings were consistent with those of MRT.

Optimal treatment for this tumor has not been established. Our case may be useful in defining treatment for MET.


Copyright © 2000, Igaku-Shoin Ltd. All rights reserved.

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電子版ISSN 1882-1251 印刷版ISSN 0301-2603 医学書院

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