黄斑上膜を伴う網膜剥離を呈した片眼性の家族性滲出性硝子体網膜症の1例

Retinal detachment with epiretinal membrane in a case of unilateral familial exudative vitreoretinopathy

（18-P1-12）　17歳女性が左眼の網膜剥離で受診した。矯正視力は右0.1，左0.06で，それぞれ−6Dと−8Dの近視があつた。左眼底には鼻側を除き扁平な網膜剥離があり，後極部に黄斑上膜，牽引乳頭，網膜血管の走行異常，周辺部に広範な無血管野と新生血管があった。螢光眼底造影で，後極部に網膜血管の直線化と多分岐があり，鼻側以外の赤道部に新生血管からの色素漏出があった。硝子体手術で左眼網膜剥離は復位し，矯正視力は1.0になり，視野も改善した。

A 17-year-old female was referred to us for retinal detachment in her left eye. The corrected visual acuity was 0.1 right and 0.06 left. Myopia of -6D and -8D was present. The left eye showed extensive flat retinal detachment except the nasal hemisphere. Epiretinal membrane, tracted optic disc and abnormalities in retinal vascular structure were present in the posterior pole. Wide avascular zone and neovascularizations were present in the periphery. Fluorescein angiography showed linear course of retinal vessels and supernumerous bifurcations. Dye leakage was prominent from newly formed vessels in the equator except the nasal hemisphere. Vitreous surgery induced reattachment of the retina. The corrected visual acuity recovered to 1.0 with improved visual field.