Clinical manifestations of familial exudative vitreoretinopathy associated with rhegmatogenous retinal detachment Yoshiko Okubo 1 , Akira Okubo 1 , Yuka Shimizu 1 , Sadao Kanagami 1 , Hiroyuki Shimizu 1 1Dept of Ophthalmol Jichi Med Sch pp.1763-1767
Published Date 1989/10/15
DOI https://doi.org/10.11477/mf.1410211035
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Clinical and genealogical studies of rheg-matogenous retinal detachment (RRD) led to the detection of familial exudative vitreoretinopathy in 58 members in 19 families. The state of FEVR in the intial 19 eyes with RRD was classified as periph-eral avascular type in 16 eyes (84%), as dragged disc type in 2 (11%) and as congenital retinal fold type in 1 (5%). We then evaluated the state of FEVR in the group excluding the 19 patients with RRD. Out of 78 eyes of 39 subjects, 66 eyes (85%)were assigned to the peripheral avascular type, 7 (9%) to the dragged disc type and 3 (4%) to the congenital retinal fold type. Sixteen eyes in these eyes (21%) showed pathological findings predispos-ing to RRD : retinal breaks in 13 eyes, RRD in 1 and past history of RRD in 2.

Fluorescein angiography was performed in 12 out of the 19 eyes with RRD. The retinal breaks were located in the avascular peripheral retina just peripheral to the line of demarcation.

The findings point to the importance of periph-eral avascular type of FEVR as one of the major causes of RRD.

Copyright © 1989, Igaku-Shoin Ltd. All rights reserved.


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