Sturge-Weber症候群に合併した脈絡膜血管腫の2例

Choroidal hemangioma and serous retinal detachment in two cases of Sturge-Weber syndrome

要約　目的：漿液性網膜剝離が脈絡膜血管腫に併発したSturge-Weber症候群2症例の報告。症例と経過：それぞれ7歳男児と15歳男性で，出生時にSturge-Weber症候群と診断されている。いずれも片側の三叉神経第1枝の領域に血管腫があり，同側の眼底に脈絡膜血管腫があった。1例は17年間，ほかの1例は12か月間の経過を追った。1例には漿液性網膜剝離が生じ，矯正視力は初診時の0.6から光覚弁に低下した。ほかの1例では漿液性網膜剝離が増減を繰り返した。結論：Sturge-Weber症候群に併発する漿液性網膜剝離は特発性に増減し，視力が低下することがある。

Abstract.　Purpose：To report 2 cases of Sturge-Weber syndrome that manifested choroidal hemangioma with serous retinal detachment. Cases and Findings：Both were males and were aged 7 and 15 years initially. Both were diagnosed with Sturge-Weber syndrome during infancy. They showed unilateral portwine hemangioma in the area of first branch of the trigeminal nerve. Choroidal hemangioma was present in the ipsilateral fundus. One case was followed up for 17 years and the other for 12 months. One case developed serous retinal detachment with initial visual acuity of 0.6 down to light perception. Retinal detachment in the other case showed fluctuations during follow-up. Conclusion：Serous retinal detachment in Sturge-Weber syndrome may spontaneously fluctuate associated with changing visual acuity.