視神経部分低形成の7例

Seven cases of segmental optic nerve hypoplasia

要約　目的：視神経部分低形成と診断した7症例の報告。症例と方法：7例9眼を視神経部分低形成と診断した。いずれも緑内障専門医が経過観察中の患者であり，男性1例，女性6例で，年齢は23～77歳（平均48歳）であった。診断は視野欠損の形態と，Kimら（1989年）が提唱した眼底所見に基づいて行った。所見：全例に母親の糖尿病歴はなく，6例が近視眼であった。4例に緑内障としての治療歴があり，うち3例は緑内障，1例は高眼圧であった。低形成の部位は，上方3眼，鼻側4眼，上方と鼻側の合併が2眼であった。結論：視神経部分低形成は乳頭上方以外にも生じ，緑内障の併発が多い。

Abstract.　Purpose：To report seven cases of segmental optic nerve hypoplasia. Cases and Method：Nine eyes of 7 patients were diagnosed as segmental optic nerve hypoplasia. All were being followed up by a glaucoma specialist. The series comprised 1 male and 6 females. The age ranged from 23 to 77 years,average 48 years. The diagnosis was made on characteristic shape of visual field defect and fundus findings described by Kim et al（1989）. Findings：Maternal diabetes mellitus was absent throughout the series. Six cases were myopic. Four cases had been treated as glaucoma. Further studies identified 3 cases as glaucoma and 1 case as ocular hypertension. Optic nerve hypoplasia was located superiorly in 3 eyes,nasally in 4 eyes,and superior-nasally in 2 eyes. Conclusion：Segmental optic nerve hypoplasia may involve superior and other sector of the disc. Glaucoma may often accompany this condition.