A Case of Hirayama's Disease Successfully Treated by Anterior Cervical Decompression and Fusion Hirotoshi Imamura 1 , Shigeo Matsumoto 1 , Makoto Hayase 1 , Yoshifumi Oda 1 , Haruhiko Kikuchi 1 , Makoto Takano 2 1Department of Neurosurgery, Kobe City General Hospital 2Department of Neurology, Kobe City General Hospital Keyword: flexion myelopathy , Hirayama's disease , juvenile muscular atrophy of unilateral upper extremity , magnetic resonance imaging , surgical treatment pp.1033-1038
Published Date 2001/11/1
DOI https://doi.org/10.11477/mf.1406901863
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The authors report the case of a 16-year-old boy with Hirayama's disease (juvenile muscular atrophy of unilateral upper extremity). The present history began about 6 months previously, when he noticed slowly progressive weakness with atrophy of the left hand and forearm. Neurological examination on admission revealed diffuse distribution of muscular atrophy in-cluding the left hypothenar, thenar, forearm, and tri-ceps muscles. However, EMG studies identified neuro-genic changes in both upper extremities. There was no long tract sign of objective sensory impairment.

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