von Recklinghausen’s diseaseに合併したCystic pontine gliomaの1例

Cystic Pontine Glioma Associated with von Recklinghausen's Disease:Report of a case

I．はじめに

　gliornaの多くは実質性，浸潤性であり，特にpontine　gliomaはその局在からも一般に手術適応外におかれ，化学療法や放射線療法に頼らざるを得ない状況にあった．しかし，high resolution CTの出現により，腫瘍の性質，すなわち実質性か嚢胞性かが判別可能となり，後者の場合には嚢胞内容の除去のみでも症状の改善さらには延命効果が期待され，手術適応と考えられる．われわれはvon Recklinghausen病に合併したcystic pontine　gliomaに対し嚢胞の開放術を行い著明な症状の改善が得られた1例を報告する．

Pontine gliomas have been considered to be out of indication for operative treatment. However, in case of a cystic type, evacuation of the cyst alone can pos-sibly extend the survival time of the patient. Since the advent of high resolution CT the nature of the pontine tumor, whether cystic or solid, can be easily differentiated, and cystic ones subjected to operation will be increasing in number. We report a case of cystic pontine glioma associated with von Reckling-hausen's disease. The patient showed a remarkable improvement in her neurological status after evacuation of the cyst.