あけお眼科医院における網膜色素変性患者の臨床的特徴

Clinical features of patients with retinitis pigmentosa attending the Akeo Eye Clinic

要約　目的：あけお眼科医院に通院中の網膜色素変性患者の現状と問題点の報告。

対象と方法：過去11年間に来院したことがある網膜色素変性患者95例を検索した。男性51例，女性44例で，年齢は13〜78歳，平均48歳である。矯正視力，Humphrey視野，Goldmann視野などを評価した。

結果：初診時の年齢は40歳代が25例と最も多かった。40歳代では6例で右眼または左眼視力が0.01以下であり，Humphrey視野のMD値が−31dB以下が右眼9例，左眼11例と多かった。視機能良好例では，視力0.7以上が50歳代では右眼10例，左眼11例にあり，視野−27dB以上が60歳代では右眼8例，左眼9例にあった。95例全例では，視力障害による身体障害1級相当が11例，2級相当が6例にあり，視野障害による2級相当が35例にあった。当院では21例に障害年金，16例に身体障碍者等級の診断書を発行した。

結論：網膜色素変性による視機能不良例は40歳代に集中し，視機能良好例は50歳代と60歳代に多かった。本症患者については，障害年金と身体障碍者の診断書発行について留意する必要があった。

Abstract　Purpose: To report the current status and problems of patients with retinitis pigmentosa（PR）attending the Akeo Eye Clinic.

Cases and Method: This retrospective study was made on 95 PR cases who were seen by us in the past 11 years. The series comprised 51 males and 44 females. The age ranged from 13 to 78 years, average 48 years. They were evaluated regarding best-corrected visual acuity, and Hymphrey and Goldmann perimetry.

Results: There were 25 patients in the 5th decade and formed most numerous age group. There were 6 patients among the 25 cases who had visual acuity of 0.01 in either eye. MD value by Humphrey perimetry was −31 dB in 9 right eyes and 11 in the left. Out of cases in the 7th decade, MD value was −27 dB or over in 8 right eyes and in 9 left eyes. In the whole 95 cases, 11 and 6 cases each were evaluated as grade 1 or 2 respectively with visual impairment. Visual field defect was evaluated as grade 2 in 35 cases. We issued medical certificates for pensions to 21 cases and for visual disability

Conclusion: Visual disability due to PR was most frequent in the 5th decade. It was less frequent in the 6th and 7th decade. Patients with PR had to be assessed regarding medical certificates for visual disability.