先天性全色盲眼の螢光眼底像と視覚誘発反応

Fluorescence Fundus Angiography, Visually Evoked Cerebral Potential and Autocorrelogram of EEG in a Case with Congenital Total Color Blindness

緒言

　先天性全色盲（ここでは桿体一色型）は単に顕著な色覚異常のみでなく，中心視力障害，眼振，差明を合わせ伴い，かつ部分色盲とは異なつた遺伝形式^1）であるということから，多くの研究者の興味をそそり，種々の研究が行なわれてきた。特に光覚，色覚に関しての報告は数多い。今回われわれは，典型的な先天性全色盲患者に，近年その診断的価値が重視されてきた螢光眼底写真像と，視覚誘発反応（VEP）を求め，興味ある結果を得たので，その他の成績とあわせ報告する。

Various examinations were carried out on the visual system of an eighteen-year-old male with congenital total color blindness (rod-monochro-matism).

(1) A change suggesting Kohlrausch's win-ding (cone-rod break) was observed in the dark adaptation curve during mydriasis (Fig. 5-B).

(2) The oscillatory potential in the ERG of this case was considerably less than normal (Fig. 6-A).

(3) The macular dark spot in fluorescence fundus angiography is not necessarily due to normal cones, since it was also observed dis-tinctly in this case like in a normal subject.