網膜血管形成異常の1例

Developmental delay of the retinal vessels. A case report

　在胎34週，生下時体重1,850gの男児の片眼に認められた網膜血管形成異常の1例につき報告した．本症例はCoats'病，未熟児網膜症，　familial exudative vitreoretino-pathyおよびこれに類似の硝子体網膜症と類似点をもち，網膜血管の発育異常に起因する一連の疾患群に属するものと考えられた．

We observed a 3-year-old male child with developmental delay of retinal vessels in the right eye. The infant was born after 34 weeks gestation weighing 1,850g. He received no oxygen therapy and was free of other congenital defects. Family history was uneventful.

We detected telangiectasis in the temporalretina and a wide avascular area in the periphery in the right eye at 11 weeks. The left eye was normal. Photocoagulation was applied to the telangiectatic area at 16 weeks. After the treated area improved, telangiectasis gradually appeared in the other retinal areas accompanied by white exudates along retinal vessels. No capillary micro-aneurysms had formed during the 2-year follow-up period. Mild telangiectasis and leakage of retinal vessels were seen by fluorescein angiography. While this case showed some similar features with ret-inopathy of prematurity, Coats' disease, familial exudative vitreoretinopathy and other hereditary vitreoretinopathies, it has not been possible to pinpoint the diagnosis.