先天性中耳真珠腫の2症例

Congenital Cholesteatoma: Report of Two Cases

I．はじめに

　鼓膜穿孔のない真珠腫は，本邦でも度々報告があるが^1），今回われわれは，末梢性顔面神経麻痺を主訴とし，鼓膜穿孔および中耳炎の既往なく，諸所見から先天性真珠腫と思われた2症例を経験したので報告する。

　Case 1. A 28-year-old male complained of left facial palsy of gradual onset. The examination showed ipsilateral profound sensorineural deafness and loss of caloric response without any perforation of the left tympanic membrane or otorrhea. The operation revealed a large cholesteatoma originating in the petrous pyramid.

　Case 2. A 21-year-old female was examined because of right facial palsy of gradual onset and ipsilateral facial spasm. The examination showed a right conductive hearing loss and a whitish mass behind an intact tympanic membrane. The operation revealed a cholesteatoma occupying the epitympanum.