Transsphenoidal Meningoencephaloceleの1例

A Case of Transsphenoidal Meningoencephalocele

I．はじめに

　頭蓋底髄膜瘤は，35000の出生ごとに1例の割合で発生するとされている稀な疾患であり，その病態や治療法は未だ確立されていない．今回，われわれは頭蓋底髄膜瘤の中でも治療成績が不良とされるtranssphenoidaltypeの頭蓋底髄膜瘤の1例を経験したので報告し，その手術適応について若干の文献的考察を加えた．

A 6-year-old boy was sent to us due to basal meningo-encephalocele detected by MRI. He had had a past history of strabismus and morning glory syndrome since 6 months of age, as well as hypopituitary dwarf-ism since he was 3 years old.

On admission, physical examination revealed hyper-telorism and left coloboma. Laryngoscopic examination revealed a round mass covered by normal nasal mucose in the midline of the tegmen of the choana. X-ray tomo-gram and CT scan demonstrated an isodense mass protruding into the nasopharyngeal cavity through a bony defect of the sella turucica.