肺動静脈瘻を合併した脳動静脈瘻の1手術例—Hereditary hemorrhagic telangiectasiaとの関連について

Cerebral and Pulmonary Arteriovenous Fistula with Possibie Hereditary Hemorrhagic Telangiectasia: Case report

I．はじめに

　脳動静脈奇形，脳血管腫などの先天性脳血管病変において，他臓器に血管異常を合併することは稀である．今回われわれは，右頭頂葉脳動静脈瘻の患者で，肺動静脈瘻を合併した症例を経験したので，若干の文献的考察を加え報告する．

Hereditary hemorrhagic telangiectasia (Rendu-Osler-Weber disease) is a syndrome characterized by the presence of mucocutaneous telangiectasia, recurrent hemorrhage (epistaxis from nasal telangiectasia is by far the most common form), and hereditary occur-rence. Hereditary hemorrhagic telangiectasia is thought not to be a simple mucocutaneous disease but a generalized vascular dysplasia, because multiplevisceral organs and systems, including central nervous system, are involved. But, an involvement of the central nervous system in this disease is rare.