Spontaneous Cerebral Ventriculostium

Spontaneous Cerebral Ventriculostium

Ⅰ．はじめに

　Spontaneous cerebral ventriculostium^5，16）は，W．H．Sweetが1940年に発表して以来，別名spontaneous（cerebral）　ventriculostomy^{4，9，10，17，19）}，spontaneous rupture of the cerebral ventricle^14，18），cyst or cystic expansion of the suprapineal recess^{1，8，12）}，またはdiverticula or diverticulum^{3，5，6，11）}等の表現で，欧米の文献には約40例が報告されている（Table 1）．

　ventriculostiumとは，側脳室または第Ⅲ脳室がおもにaqueduct以下の髄液通過障害のために拡大し，解剖学的に弱い部分から脳表に向って拡張し，脳室上衣およびクモ膜をかぶった嚢腫様の形でherniateした状態を指す．

Two cases of spontaneous cerebral ventriculostium are presented. The first case is that of a 3 year-old girl with a thumb-sized soft scalp tumor of the occipital region (dural hypertrophy) and hydroencephalodysplasia (Picaza). PVG revealed noncommunicating hydrocephalus with asymmetrical deformity of the lateral ventricle and agenesis of corpus callosum (Fig. 1). Ventriculoatrial shunt was performed. Three years passed under the useful life when she readmitted to our clinic complaining headache, nausea and vomiting.