蝶形色素沈着黄斑ジストロフィに似た蛍光眼底造影所見を呈した黄斑ジストロフィの1例

A case of macular dystrophy resembling butterfly-shaped pigment dystrophy of the fovea

　蝶形色素沈着黄斑ジストロフィは黄斑部網膜色素上皮に特異な暗い色素沈着を認め，検限鏡所見からほぼ確実に診断できる黄斑ジストロフィとされているが，きわめて稀な疾患である。47歳の白人男性で両限に特異な病巣を有し，その螢光眼底造影所見が蝶形色素沈着黄斑ジストロフィに似た黄斑ジストロフィの1例を報告した。

The patient was a 47-year-old Caucasian male.Visual acuity was slightly affected in his right eye.Relative central scotoma was detected by Gold-mann perimetry and diminished central sensitivity was demonstrated by static campimetry using the Sargon program of Octopus. Color vision was nor-mal and the light-dark ratio of EOG was normal.

Ophthalmoscopy revealed a butterfly-shaped and yellow-white lesion in the macular area of his right eye and a butterfly-shaped or geographic pattern and yellow-white lesion in the posterior pole of his left eye.