Hydroencephalodysplasia 3例の手術経験について

THREE CASES OF HYDROENCEPHALODYSPLASIA:Successful Surgical Treatment

I．はじめに

　HydroencephalodysplasiaはPicazaにより命名された先天性奇形であり，hydrocephalusの一部に含まれるものである。

　病理解剖学，診断，治療，予後などの面でhydroen—cephalodysplasiaは普通のいわゆるhydrocephalusとは明らかに区別されるものであるが，最近われわれは本疾患3例を相ついで経験し，外科的治療を行なつたので報告する。

Three cases of hydroencephalodysplasia were report-ed. Hydroencephalodysplasia is one of the congenital malformations, and is characterized by increased intra-cranial pressure and dysplasia of the brain. This malformation will be discovered among the cases of hydrocephalus in a fairly large number if we will keep our mind on the presence of the disease.

In our cases, angiography revealed most characte-ristic findings, and transillumination was useful in diagnosis of the disease.

By using ventriculoscope in one of our cases, we could see directly the defect of the brain without lar-ge craniotomy which might make the patient's condi-tion worse.

Subarachnoid-atrial shunting was performed upon all three cases with satisfactory results.