脊髄延髄空洞症

A Case of Syringomyelobulbia

緒言

　脊髄空洞症に関し諸外国では幾多の報告，記載^1）2）3）があるが，本邦に於ける例は比較的少く，昭和27年迄50数例^4），其後の報告例を併せても，70例に満たない。そのうち延髄，間脳症状を伴う例は意外に少く20例に満たず，それも死亡前短期間の観察であることが多い。吾々は最近，初期より眼球振盪を認め，脊髄空洞症の症候増悪とともに種々の延髄症候を示した脊髄延髄空洞症の一例を経験したので以下に報告する。

The authers reported the case of a 28 years old female who developed the syndrome of Syringomyelia accompanied with nystagmus and other bulbary symptoms.

From the onset of the disease the patient suffered from photophobia, dizziness, diplopia and weakness of the left upper extremity. There was a relatively slow progression of symptoms during the subsequent 13 years, until she started to complain of difficulty of the gait, tremor of the left hand, headache, bussing in the ears, nausea, vomiting, pers-piration and dyspnea.

The examination revealed the following positive findings:

bilateral Horner's syndrome, pendular nys-tagmus upon forward gaze and rotator Nys-tagmus upon lateral gaze, slow and nasal speach, atrophy and fascicular twitches of the tongue and the left thenar eminence, involuntary movements of the fingers of the left hand, dorsal Scoliosis, several scars due to burnings on the left forearm and the fin-gers of the left hand, hyperactive biceps and trices reflexes of the right but the negative reflexes of the left, hyperactive Knee and ankle reflexes, slightly positive Babinskis reflex and spastic-atactic gait.