Intestinal Lymphangiectasia Kunihiko Aoyagi 1 , Koichi Eguchi 1 , Mitsuo Iida 2 1Department of Gastroenterology and Medicine, Faculty of Medicine, Fukuoka University, Fukuoka, Japan 2Department of Medicine and Clinical Science, Graduate School of Medical Sciences, Kyushu University, Fukuoka, Japan Keyword: 腸リンパ管拡張症 , 蛋白漏出性腸症 , 小腸内視鏡 , α1アンチトリプシン・クリアランス試験 , 脂肪制限 pp.667-671
Published Date 2008/4/24
DOI https://doi.org/10.11477/mf.1403101347
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 Intestinal lymphangiectasia is a disease characterized by a dilatation of lymphatics, which leads to the loss of lymph to the intestine. Clinical symptoms and signs include edema, diarrhea, steatorrhea, abdominal pain, chylous ascites and pleural effusion, hypoalbuminemia, hypocalcemia, peripheral lymphocytopenia, and an increased susceptibility to infection. Diagnosis can be established by endoscopic findings such as white villi, white spots, white nodules, and submucosal elevations, and the evidence of protein-losing enteropathy, which is confirmed by the alpha 1-antitrypsin clearance test and 99mTc-human serum albumin scintigraphy. Lymphangiography and lymphoscintigraphy are also of value. The principle for the treatment of this disease is the restriction of oral fat intake, although underlying problems should also be treated in secondary disorders.

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