cardio-facio-cutaneous症候群患児の腹腔鏡下胃瘻造設術に対する全身麻酔経験

A Case of Cardio-facio-cutaneous Syndrome Undergoing Gastrostomy under General Anesthesia

要旨

　cardio-facio-cutaneous症候群の13歳の男児に対して腹腔鏡下胃瘻造設術が予定された。筋弛緩モニター下に筋弛緩薬の投与を行ったが，筋弛緩薬の効果発現は遅く，作用遷延もなかった。スガマデクスにより速やかな筋弛緩状態からの回復が得られた。懸念された術後呼吸器合併症を起こすことはなかった。

　Cardio-facio-cutaneous syndrome is a rare condition characterized by craniofacial features, congenital heart disease, seizure, musculoskeletal manifestation, growth retardation and intellectual disability. These conditions may significantly impact patient perioperative outcomes.

　We describe a case of 13 year-old child with cardio-facio-cutaneous syndrome who has a need of feeding tube for a long term. Gastrostomy was scheduled under general anesthesia using muscle relaxant with neuromuscular monitoring. The onset of muscle relaxant was delayed and the duration of its effect was not prolonged. Furthermore, rapid recovery of muscular function was gained with sugammadex.

　No postoperative respiratory complications were observed during perioperative period in this case.