Neurofibromatosisに伴った多発性頭蓋外椎骨動脈瘤の1例

A Case of Multiple Extracranial Vertebral Artery Aneurysms Associated with Neurofibromatosis

I．はじめに

　Neurofibromatosisに合併する頭蓋外椎骨動脈瘤は稀な疾患であるが^2,3,5-11），われわれはその多発例を経験したので，文献的考察を加え報告する．

An unusual case of multiple aneurysms of the ex-tracranial vertebral artery associated with neurofibro-matosis is presented.

A 48-year-old woman, complaining of weakness and numbness of the left upper extremity, was admitted to our hospital on July 27, 1987. She had undergone the removal of a left internal thoracic artery aneurysm due to hemothorax on June 12, 1987. On the next day, the symptoms of the left upper extremity appeared.

On admission, general physical examination showed multiple cafe-au-lait spots on her body and cervico-thoracic scoliosis. Neurological examination revealed left C5, 6 radiculopathy. Cervical CT scans showed en-hanced masses at the transverse foramina. Left subcla-vian angiography demonstrated multiple extracranial vertebral artery aneurysms from the origin of the ver-tebral artery to the C4 level.

This case was treated by proximal and distal ligation of the aneurysms. Postoperative right and left angio-grams revealed no aneurysms filled with contrast mate-rials. The weakness and numbness of the left upper ex-tremity disappeared gradually after the operation.