Neurological Surgery No Shinkei Geka Volume 46, Issue 1 (January 2018)

A Case of Primary Intracranial Epithelioid Hemangioendothelioma Fukuko YAMAMOTO 1 , Hironori YAMAGIWA 1 , Fuminori IWAMOTO 1 , Tsutomu KASUGAI 2 1Department of Neurosurgery, Japan Community Health care Organization(JCHO)Osaka Hospital 2Department of Pathology, Japan Community Health care Organization(JCHO)Osaka Hospital Keyword: epithelioid hemangioendothelioma , primary brain tumor , convulsion pp.35-40
Published Date 2018/1/10
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 Epithelioid hemangioendotheliomas(EHEs)most commonly occur in the liver, lung, bone, and soft tissues, but rarely in the brain. Here, we describe a case of primary intracranial epithelioid hemangioendothelioma manifested by an epileptic attack.

 A 53-year-old woman with no previous convulsive history presented at our hospital after experiencing a seizure. Magnetic resonance imaging revealed a mass in her right frontal lobe, with edema, which was well enhanced with gadolinium. Systemic computed tomography, on the other hand, did not show any tumor involvement in other organs. The patient underwent surgery, and a complete resection of the intracranial tumor was successfully performed. The histological diagnosis was an EHE. There was no evidence of tumor recurrence either in the brain or other organs at 3 years and 7 months after surgery.

 Because of its rarity, the exact prognosis of patients with an intracranial EHE has not been clearly established. Moreover, tumor recurrence following complete resection has been reported and thus regular follow-up examinations are considered necessary.

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Neurological Surgery 脳神経外科
46巻1号 (2018年1月)
電子版ISSN 1882-1251 印刷版ISSN 0301-2603 医学書院