Syringomyeliaを伴った頸髄髄外腫瘍の1例

An Extramedullary Spinal Cord Tumor Associated with Syringomyelia: A case report

I．はじめに

　Gardner^5）の報告以来，脊髄空洞症は脊髄の変性疾患でなく，その多くがChiari奇形の二次的変化であることは，疑いのないこととなった．また，脊髄空洞症の主要な原因として，脊髄髄内腫瘍があることも今日では周知のことである^1）．しかし，脊髄髄外腫瘍に脊髄空洞症が合併したという報告は，極めて少ない．

　われわれは，17年前に発症し，その後平山氏病と診断され，神経脱落症状が徐々に進行してきたため，その時々に脊髄撮影，CT,MRIなどの検査を受けてきた症例を経験した．

A 53-year-old woman presenting weakness in the left hand for ten years was diagnosed seven years ago as having juvenile muscular atrophy of the unilateral up-per extremity. Afterwards, her left forearm and hand gradually became weaker. A neurologist pointed out syringomyelia in the film of MR imaging. However, the cause of syringomyelia was not demonstrated until gadolinium-DTPA-enhanced MR imaging disclosed a spinal tumor. Through an operation it was found that it was an intradural extramedullary tumor at C7 level. Histological diagnosis of the tumor was meningioma.