Epidermolysis Bullosa Hereditaria Letalis（Herlitz）—症例報告

　Epidermolysis bullosa hereditaria letalis^1）（以下E. letalisと略）については，われわれ^2）は前に1例を報告した。ここでは，その後に観察した本症の1例および類似例（1例）を述べ，若干の考察を加える。

　Two cases of this disease treated with almost the same procedures were reported.

　Case 1 : Epidermolysis bullosa hereditaria dystrophica et polydysplasia. He survived until the age of 7 years and 6 months. The basement membrane at the bullous lesion was proved to be attached to the epidermis by the light- and electron-microscope.

　Case 2 : Epidermolysis bullosa hereditaria letaris. He died at the age of 6 months. The basement membrane was proved to be attached to the dermis by the light microscope.

　The results of histological studies on the location of the basement membrane at the bullous lesion of the already reported cases of this disease from Kanazawa University were discussed.

　The discussion and review on the relationships between the histological locations of the bullae and the prognosis of the patients were performed.