同胞にみられたpigmented paravenous retinochoroidal atrophy

Pigmented paravenous retinochoroidal atrophy in siblings

（1） pigmented paravenous retinochoroidal atrophyの同胞の2症例を報告した。

（2）兄は両眼に，弟は片眼に乳頭周囲よりヒトデ状に網膜血管とくに静脈に沿って網脈絡膜萎縮と色素沈着を認めた。

（3）螢光眼底所見から病巣は脈絡膜毛細血管の閉塞と網膜色素上皮層の萎縮がみられ，脈絡膜循環障害が本症発症に重要な因子であると考えられた。

（4）本疾患を遺伝性疾患として検討する必要性について述べた。

We observed pigmented paravenous retinochoroi-dal atrophy in a pair of brothers, aged 11 and 14 years respectively. The condition was bilateral in the elder brother and was unilateral in the younger. Electroretinogram and dark adaptation tests were normal. Fluorescein angiography showed findings suggestive of circulatry disturbance in the choroidal capillaries and atrophy of retinal pigment epithe-lium. These observations seemed to support the view that the origin of the disease is located at the level of choriocapillaris and that the pigmented paravenous retinochoroidal atrophy is hereditary in nature.