首をねじり横目でないとものを注視出来ない症例

Congenital ocular motor apraxia

　Cogan^1）は核上障碍による眼球共同運動麻痺の中，随意運動のみが障碍されている例を区別し，先天性の4症例をあげて先天性眼球運動失行症Congenital ocular motor apraxiaと呼んだ。本症と思われる2例を経験したので追加報告する。

Two cases of congenital ocular motor apraxia (Cogan) were reported. The one was 3 years and 7 months old girl with divergent squint, whose mother and brother had a typical eccentric nystagmus. The other was a boy, aged 10 months.

Both cases presented remarkable ocular apraxia, that is, inability of voluntary and com-mand movements of the eye in horizontal plane, and preservation of involuntary movements and proprioceptive reflexes. When they attempted to fixate an object held in front of them, the eyes presented something like conjugate deviation, being accompanied by a char-acteristic conpensatory jerky head movement.