先天性停止性夜盲症の1異型（いわゆる斑紋眼底）のEOGおよびVEP

EOG and VEP of "Fleck Retina with Congenital Nonprogressive Nightblindness"

I．緒言

　1959年，神鳥^1）はまだ記載のなかった先天性停止性夜盲の1異型を発表し，これを斑紋眼底（以下fleck reti—na）と呼んだ。以来神鳥ならびにその共同研究者^2）〜9）によつて，眼底所見，ERG，螢光眼底像，およびその他の諸検査成績の詳細が報告されて，欧米においてはfleckretina （Kandori）と呼ばれている^{10）〜15）}。

　今回，10数年観察するも停止性の1症例にEOGならびにVEP的検索を行なつたので，ERG所見とともにここに報告する。

One case of "fleck retina with congenital non-progressive nightblindness" in a female subject born in 1926 has been followed up for over 10 years. This condition could be differentiated from other nightblind cases and the so-called flecked retina syndrome through electrophysiological studies with EOG (electro-oculogram) and VEP (visually evoked potential).

The EOG findings were normal with the dark trough time of 15 min. OD and 13 min. OS. The light peak time was 9 min. OD and 11 min. OS. The d value which signifies light peak-dark trough was 140μV OS and 240μV OS.