Idiopathic juxtafoveolar retinal telangiectasis group 2Aの1例

A case of idiopathic juxtafoveolar retinal telangiectasis group 2A

要約　目的：Idiopathic juxtafoveolar retinal telangiectasis group 2Aの症例の報告。症例と所見：53歳女性が2年前からの視力低下で受診した。矯正視力は右0.2，左0.4であり，両眼の黄斑耳側に灰白色混濁があった。右眼には軽度の網膜下出血と混濁部の隆起，左眼にはクリスタリン様沈着物があった。フルオレセイン蛍光眼底造影で色素漏出を伴う毛細血管網の拡張があり，特発性傍中心窩末梢血管拡張症第2群と診断した。光干渉断層法（OCT）検査で両眼に視細胞層の途絶とlamellar cystがあった。右眼にトリアムシノロンをテノン囊下に投与し白色隆起病変が瘢痕化したが，視力は変化しなかった。網膜下血管新生の存在が疑われた。結論：本症での視力低下には網膜の萎縮性変化が関与している可能性がある。

Abstract.　Purpose：To report a case of idiopathic juxtafoveolar retinal telangiectasis group 2A. Case and Findings：A 53-year-old woman,presented with blurring of vision since 2 years before. Her corrected visual acuity was 0.2 right and 0.4 left. Both eyes showed area of grayish opacity temporal to the macula. The right eye showed,additionally,elevation of opaque area with subretinal hemorrhage. The left eye showed crystalline deposits. Fluorescein angiography showed dilated capillaries with dye leakage temporal to the macula,leading to the diagnosis of idiopathic juxtafoveal telangeiectasia group 2A. Optical coherence tomography（OCT）showed disruption in photorecepter layer with lamellar cyst. The elevated opaque lesion in the right eye became atrophic following subtenon injection of triamcinolone. There was no change in visual acuity. The finding was suggestive of subretinal neovascularization. Conclusion：Impaired visual acuity in this clinical entity may be associated with atrophic changes in the retina.