Torsionsdystonie （od． Torsionsdystonischer Symptomenkomplex）の1臨床例について

A CASE OF TORSIONSPASM

I．緒言

　躯幹を中心とする特有な捻転運動と筋緊張の亢進・減退の交代を主徴候とし，錐体外路性症候群の1つと考えられるTorsionsdystonieについて，西欧に於てはSchwalbe （1908）以来^1），我国に於ては荒木（大正13年）以来^3）〜19）の諸報告があるが，その症例は比較的僅少であつて，我国において現在までに報告されたものは十数例を数えるに過ぎない。

　私は昨年来，本症の比較的軽症と思われる1例を経験したので此処に報告する。

A mild case of Tortionspasm is reported and discussed.

The patient is a 14 years old Japanese girl who has been afflicted since the age of ten. She first noted characteristic involuntary movements when she started to run at an athletic meeting. Since the original attack the involuntary movements come when she moves suddenly in situation where there is tension or emotional shock. She just becomes stiff and all motion ceases for a few seconds. This is followed by a show twisting of the upper part of the body, arm and head.

She has never lost consciousness during the attack.

Hysteria, Athetose double, Chorea minor and Pseudosclerosis were ruled out on the basis of clinical findings.

In Japan, since S. Araki reported the first case in 1924, about 15 cases of this disease have been reported. A case reported by S.Nakagawa in 1931 presented with involuntary movements associated with sudden voluntary movements. My case seems to milder than that one.