雑誌文献を検索します。書籍を検索する際には「書籍検索」を選択してください。

検索

書誌情報 詳細検索 by 医中誌

Japanese

A Case of Myotonic Dystrophy Associated with Complete Atrioventricular Block Satoshi Kojima 1 , Tetuya Ooigawa 1 , Kouichiro Aihara 1 , Yoriaki Mineda 1 , Satoru Suwa 1 , Yasumasa Fujiwara 1 , Masataka Sumiyoshi 1 , Yasuro Nakata 1 1Department of Cardiology, Juntendo Izunagaoka Hospital, Juntendo University Keyword: 筋緊張性ジストロフィー症 , 完全房室ブロック , ペースメーカー , myotonic dystrophy , complete atrioventricular (AV) block , pacemaker pp.721-725
Published Date 1997/7/15
DOI https://doi.org/10.11477/mf.1404901522
  • Abstract
  • Look Inside

44- year-old man, who had suffered myotonic dystro-phy for 7 years, was referred to our hospital because of complete atrioventricular (AV) block and congestive heart failure. On the first hospital day, he had polymor-phic ventricular tachycardia with QT prolongation (tor-sades de pointes), ventricular fibrillation followed by cardiac arrest. However, he was successfully resuscitat-ed with temporary pacing. His bundle electrogram revealed that the site of AV block was at the distal portion of the his bundle potential. Coronary angiogra-phy showed no atherosclerotic stenosis, but left ventriculography demonstrated diffuse hypokinesis with an ejection fraction of 53%. An endomyocardial biopsy specimen from the right ventricle showed hypertrophy of myocites with mild disarray and increased interstitial fibrosis. After implantation of a cardiac pacemaker, the medical course of the patient's life has been uneventful for 12 months.


Copyright © 1997, Igaku-Shoin Ltd. All rights reserved.

基本情報

電子版ISSN 1882-1200 印刷版ISSN 0452-3458 医学書院

関連文献

もっと見る

文献を共有