Currarino triad（直腸肛門奇形，仙骨奇形を伴う仙骨前髄膜瘤）の1例

Currarino triad:a case report

I．はじめに

　1981年にCurrarinoら^2）により報告された直腸肛門奇形，仙骨奇形，仙骨前腫瘤をtriasとする症候群はCur—rarino triadと呼ばれるが，その報告例は未だ少なく稀な疾患と考えられる．今回われわれは，直腸肛門奇形，仙骨奇形を伴う仙骨前髄膜瘤を経験したので症例を提示し，その診断，治療について若干の文献的考察を加えて報告する．

The authors report a case of Currarino triad compris-ing anorectal malformations, sacral bony anomaly and presacral mass. A 1-year-old boy was presented with constipation as his chief complaint. No neurological de-ficit was found on admission. There was no cutaneous evidence of underlying spinal dysraphism. Lumbar X-ray films showed bony defect caudal to the third sacral vertebra. A barium-enema examination revealed an anterior displacement of the rectum. A myelography showed a presacral cavity filled with contrast medium.MRI demonstrated a thick filum terminale, and a round hypointense mass in the pelvis on T1 weighted images and hyperintense on T2 weighted images. Surgically we released the thick filum terminale, and obliterated the anterior sacral meningocele, because total removal would have been hazardous. Postoperatively transient dysuria was observed for a month, and the difficulty in defecation persisted. Recognition of this rare condition will lead to correct diagnosis and proper treatment.