Currarino triadの1症例

Currarino Triad : A Case Report

　Ⅰ．はじめに

　Currarino triadは，1981年にCurrarinoら¹⁾により直腸肛門奇形，仙骨奇形，仙骨前腫瘤の3者を合併する症候群として提唱された先天異常であり，その報告例は少なく比較的稀な疾患である．今回われわれは，仙骨前腫瘤として髄膜瘤と奇形腫を合併し，tethered spinal cord を呈したCurrarino triad の1例を経験したので文献的考察を加え報告する．

　The authors report a case of Currarino triad with a combination of anterior sacral meningocele and mature teratoma,sacral body deformity,anorectal stenosis,and tethered cord. A newborn girl suffered from vomiting,abdominal distension and constipation. Initially,a diverting colostomy was performed at the age of one month. 7 months later,at the age of 8 months,we performed posterior sagittal anorectoplasty (PSARP) : As a result,extirpation of teratoma,excision of meningocele,untethering of the spinal cord,and anorectoplasty were achieved simultaneously without complication. We suggest the use of an MRI to specify the presence of anosacral and spinal cord anomalies in patients with intractable constipation and we recommend combined pediatric and neurosurgical assessment and management for all cases of Currarino triad.