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症例
脊髄動静脈奇形を伴ったKlippel-Trenaunay-Weber症候群の1症例
Spinal Arteriovenous Malformations in Klippel-Trenaunay-Weber Syndrome: Case report
唐 梃洲
1
,
高木 卓爾
2
,
永井 肇
1
En-Chow TAN
1
,
Takuji TAKAGI
2
,
Hajime NAGAI
1
1名古屋市立大学脳神経外科
2名古屋市立東市民病院脳神経外科
1Department of Neurosurgery, Nagoya City University Medical School
2Department of Neurosurgery, Nagoya City Higashi General Hospital
キーワード:
Klippel-Trénaunay-Weber Syndrome
,
Spinal arteriovenous malformation
Keyword:
Klippel-Trénaunay-Weber Syndrome
,
Spinal arteriovenous malformation
pp.877-881
発行日 1990年9月10日
Published Date 1990/9/10
DOI https://doi.org/10.11477/mf.1436900142
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- Abstract 文献概要
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I.はじめに
Klippel-Trénaunay-Weber症候群は臨床的に,1)四肢における片側性の骨格と筋肉の肥大,2)血管性母斑,3)血管系の形成異常が3大特徴とされている.この症候群のなかで血管系の形成異常として脊髄動静脈奇形を伴うことは比較的稀で,文献的には過去に19例しか報告されていない.
今回,著者らは脊髄動静脈奇形を伴ったKlippel—Trénaunay-Weber症候群の1症例を経験したので,若干の文献的考察を加えて報告する.
A 19-year-old man was admitted with the chief com-plaint of a sudden onset of thoracic pain and paraple-gia. His right lower limb had progressively enlarged since he was 3 months old. Transient paraparesis had occurred recurrently since the age of 3. Physical ex-amination on admission revealed that there were multi-ple warts on his face, trunk and right extremities. The right lower limb was thicker and longer than the left one, and the temperature was 1°C higher in the right side.
Copyright © 1990, Igaku-Shoin Ltd. All rights reserved.