"もやもや"病様症状で発症したFibromuscular Dysplasia—脳梁周囲動脈に"string of beads"像を認めた1例

A Case Report of Fibromuscular Dysplasia Presenting a Symptom like Moyamoya Disease: "String of beads" appearance of the pericallosal artery

I．はじめに

　Fibromuscular dysplasia（以下FMD）はLeadbetter^12）が腎動脈において初めて記載し，その後腹腔動脈，腸間膜動脈，頭蓋外内頸動脈，頭蓋内動脈にも同様の病変が存在することが知られている．われわれは今回"もやもや"病様症状にて発症し，血管造影にて前大脳動脈と頭蓋外内頸動脈に本症を疑わせる所見を認めた症例について報告する．

We report a case of fibromuscular dysplasia (FMD) presenting a transient ischemic attack (TIA) like Moyamoya disease. The patient, a 16-year-old woman, had recurrent attacks of right hemiparesis induced by hyperventilation. Neurological examinations revealed no abnormality. Angiography showed severe stenosis of both anterior cerebral arteries at the proximal por-tion with "string of beads" appearance in the left peri-callosal artery, and tubular stenosis of the left internal carotid artery at the level of the second cervical verte-bra. Renal artery stenosis was not seen.