Atretic cephaloceleの1例

A Case of Atretic Cephalocele

Ⅰ．は じ め に

　頭蓋骨欠損（cranium bifidum occultum）を介し頭蓋腔と頭皮下腫瘤が髄膜由来の組織でつながる先天奇形はcephaloceleと呼ばれる．この中で，囊胞を伴わないものは不全型に亜分類され^7,12)，atretic cephaloceleやrudimentary cephaloceleなどの名称で報告されてきた^2,5,10,11)．今回われわれは，straight sinus のvertical embryonic positioningを呈した頭頂部のatretic cephaloceleの1例を経験したので画像的特徴を含めた文献的考察を加え報告する．

　We report a case of atreric cephalocele. A 13-year-old boy who was developmentally normal was admitted to our hospital,complaining of scalp mass located at the midparietal region. He was noticed to have had it since his birth. Physical examination revealed 2.5×2.5cm,round,skin-covered midline subscalp mass with a hairless top. Bone 3D-CT showed bone defect at the base of the mass. MRI and MR venography showed the embryonic positioning of the straight sinus. He was treated with surgical excision of the mass,and fibrous tract extending intracranially at the base of the lesion was identified. Pathologic examination showed it to be meningocele.