先天網膜動静脈吻合の1例

A case of congenital arteriovenous communications of the retina

　感覚性外斜視で受診した26歳女性にみられた，先天網膜動静脈吻合の1例を報告した。拡張，蛇行した血管は視神経乳頭から全方向に広がり，FAでは蛇行血管の全てが直接造影された。1Aでは網膜から戻った血管が脈絡膜へ分布する様子が観察された。また，硝子体中に突出して見える拡張した血管は，OCT上では網膜内の種々の深さの低信号領域として描出された。これは先天網膜動静脈吻合で，lAおよびOCT画像の初めての報告である。

A 26-year-old woman presented with exotropia as the chief complaint. Her corrected visual acuity was nolight perception right and 1.2 left. Funduscopy showed arteriovenous communications of the retina involving all the vesselsin her right eye. The finding was compatible with the diagnosis of Wybern-Mason syndrome. Fluorescein angiographyshowed dye filling in all the affected retinal vessels. Indocyanine green angiography showed a direct communicationbetween retinal and choroidal veins. The choroidal vessels showed no remarkable malformations. Optical coherencetomography (OCT) showed multilobular lacunae located at various levels in the retina consistent with convoluted vesselsprotruding from the retina. To our best knowledge, this is the first report on this syndrome regarding the venovenousanastomosis between the retina and the choroid as well as OCT findings.