異所性松果体腫瘍の1例—経過・剖検所見

A CASE OF ECTOPIC PINEALOMA:A STUDY ON COURSE AND AUTOPSY

I．はじめに

　小児期に発病し，進行性に片麻痺がみられる異所性松果体腫瘍が，最近いくつか報告され注目されている。ほぼ典型的な経過をとり，同側大脳半球萎縮をきたし，性格変化が強く，ついにはakinetic mutisrnの型をとり死亡した，4年7カ月の全経過と臨床症状および，脳波および睡眠，剖検所見を報告する。この例は，最初から脳腫瘍を疑いながらも診断を確定するに至らず死亡した例であつて，経過を詳細に報告することは診断の上で有用と思われる。

A 17 year-old male. The right hemiparesis and hemihypoesthesia appeared at age 12 and were aggravated slowly. Dementia, character and emo-tional change, and abnormal behavior were observed at 15. At age 16, consciousness disturbance and forced laughter appeared. Last 5 month, he was in state of aknetic mutism. All clinical course of patient, died of hemorrhage in the cerebral ventricles at age 17, were 4 year 7 month.

Cerebral arteriographies and pneumoencephalo-grams revealed atrophy of the left cerebral hemi-sphere and intracranial pressure was not increased.

In autopsy, tumor localized in the hypothalamus and wand of 3rd ventricle and invaded diffusely widely white matter from frontal to occipital love and pons.

Histopathological diagnosis was two cell pattern pinealoma. In Japan, 6 cases was reported which similar brain tumor. We would like to emphasize that if we obsearved similar case, we suspect ectopic pinealoma.