先天性肺動脈狭窄症ないし形成不全症

Congenital Postvalvular Stenosis of the Pulmonary Artery and its Branches.

I．緒言

　心臓カテーテル法および造影法がroutine examina—tionとして一般に施行されるようになるにつれ，様々の心奇型の診断が生存時可能となり，またそれにつれて外科的治療も積極的に加えられるようになってきた。

　肺動脈狭窄症ないし，肺動脈形成不全症は以前からとくに病理学上注目されてきた先天性心疾患の一つであるが最近の心臓外科の長足の進歩に伴い，臨床的に血行動態という面において注目されるようになってきた。

A case of congenital stenosis of the pul-monary artery associated with atrial septal defect of 15 years female was presented and a short review of the literatures concerning to that disease was carried out.

It had been considered that the surgical procedure was not always necessary for the mild case, although it might be necessary for the cases complicated with cyanosis, dyspnca, palpitation, hemoptysis, frequently reccurent pulmonary infection and pulmonary hypertension.

In the authors'case, it was revealed that the stenosis extended bilaterally from the trunk of the pulmonary artery to peripheral demonstrated by the selective right ventricu-lography. However, we had unfortunately no effective surgical treatment for these patients and so she was dead of sepsis in the course of hospitalization with conservative treatment.