多発性毛嚢々腫症について

STEATOCYSTOMA MULTIPLEX

I．はじめに

　多発性毛嚢々腫症は，1898年BoselliniによりSteatocystici multiple follicoli pilosebaceiの名称で報告されて以来，Steatocystoma multiplex（Pringle，1899），Sebocystomatosis（Günther，1917），Folliculäre Zysten（Siemens，1923），Gruppierte Retentionsatherome（Bernstein，1931），Ölzysten（Strempel，1931），Maladie polykistique épidermique hérédetaire（Sezary et Lévy-Coblentze，1931）等々の名称で報告されてきた。一方本邦では，1922年駒屋^1）が多発性毛嚢々腫症という名称で報告して以来，その発生機序に関する考え方は別として，一般に，この名称がつかわれ多くの報告がなされているが，最近9歳男子の胸骨部より心窩部にかけて多発した毛髪を内蔵する多発性毛嚢々腫症の1例を経験したので，この機会に当科における本症の統計的観察と併せ報告する。

A 9-year-old boy had miliary, dark blue, non-follicular cysts in the lower part of sternal region. The skin over the nodules were normal. They contained a mass of many small hairs.

His past and familiar history had nothing contributive.

In the histologic picture the cysts were located in the mid and lower dermis, which had no connection with epidermis nor hair follicle. Its wall was composed of keratin layer, several layers of epithelial cells and connective tissue around them. There were underdeveloped sebaceous gland and follicular structure. Its content consisted of keratin, lipid and embryonic hair.

The characteristics of this case were as follows :

(1) The age of patient belonged to the youngest range of this disease.

(2) The cyst contained many embryonic hairs.

(3) Histogenesis of this disorder seemed to be nevoid nature, becsuse it was non-follicular.