右室巨大乳頭状線維弾性腫

A Giant Papillary Fibroelastoma in the Right Ventricle

乳頭状線維弾性腫（PFE）は，良性の原発性心臓腫瘍の約8％で，大動脈弁や僧帽弁などの左心系に多く発生する．われわれは，三尖弁または右室原発と考えられる巨大PFEを経験したので，文献的考察を加え報告する．

Papillary fibroelastoma （PFE） accounts for approximately 8％ of benign primary cardiac tumors. PFE frequently develops in the left heart system, such as the aortic valve and the mitral valve. We report a case of a giant PFE in the right ventricle. The patient was an 83-year-old woman with a history of chronic atrial fibrillation, diabetes, and hypertension. She had experienced palpitation and shortness of breath for several years. A giant mobile tumor was observed in the right ventricle by transthoracic echocardiography, and its extirpation was performed. Intraoperatively, a giant tumor of 3 cm in diameter was observed on the right ventricular side of the posterior tricuspid leaflet. As the tumor strongly adhered to the tendinous cords, it was unavoidable to resect the tendinous cords. Thus, a tricuspid valve repair was performed in addition to the tumor extirpation. The patient was diagnosed with papillary fibroelastoma by pathological examination.