Japanese

Repeated laparoscopic gastric local resection for incomplete Carney triad : A case report Tsuyoshi OTANI 1 , Akihiro MIKI 2 , Atsushi IKEDA 2 , Masao FUJIWARA 2 , Junji KOMORI 2 , Yasuhide ISHIKAWA 2 1Department of Surgery, Okayama Saiseikai General Hospital 2Department of Gastroenterological Surgery, Takamatsu Red Cross Hospital Keyword: Carney triad , GIST , LECS pp.29-36
Published Date 2020/1/15
DOI https://doi.org/10.11477/mf.4426200768
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 Carney triad, as originally described in 1977, is a combination of three tumors: gastric epithelioid leiomyosarcoma [later renamed gastrointestinal stromal tumor (GIST)], extra-adrenal paraganglioma, and pulmonary chondroma. The disorder affects mostly young women and is not familial. Zhang et al. reported that gastric lesions in the Carney triad occur in multiple nodules/multiple locations, with recurrence observed in 47% of cases. They also reported that the mean age of the patients at first gastric operation is 22 years, and the mean interval between primary and secondary surgery is 10.3 years. Therefore, it is necessary to consider the quality of life of patients when choosing a treatment strategy. A 33-year-old female with Carney triad who had undergone right upper and middle lobectomy and laparoscopic partial gastrectomy with pulmonary chondroma and GIST at the age of 25 was found to have seven stromal tumors during follow-up observation. Two tumors were resected via laparoscopic local gastrectomy. Five colonized tumors were resected as a group via laparoscopy and endoscopy cooperative surgery (LECS). Laparoscopic surgery or LECS leads to few adhesions and is a suitable technique for future surgery. By minimizing gastrectomy, it preserves the function of the stomach and allows performing multiple stomach-preserving surgeries depending on patient preference.


Copyright © 2020, JAPAN SOCIETY FOR ENDOSCOPIC SURGERY All rights reserved.

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電子版ISSN 2186-6643 印刷版ISSN 1344-6703 日本内視鏡外科学会

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