Marfan症候群に併発した仙骨部Meningeal Cystの1例

A Case of Sacral Meningeal Cyst with Marfan Syndrome

I．はじめに

　最近本邦でも脊髄の嚢胞性病変の分類で，me-ningeal cystの概念が普及しつつあり，またMRIの普及で容易に診断できるようになっている，今回は結合織に異常があることが指摘されているMarfan症候群に合併する仙骨部meningeal cystの手術例を経験したので文献的考察を加え報告する．

A rare case of sacral meningeal cyst Marfan syndrome is reported. A 40-year-old male who had a pasthistory of Marfan syndrome was admitted to Tokyo Metropolitan Ebara Hospital due to sensory distur-bance in the right S1-2 nerve root area on October 1998. On admission, neurological deficits were sensorydisturbance and decreased right Achilles reflex. Plain sacral X-ray was normal. Magnetic resonance imag-ing revealed a cystic mass in the intrasacral space. MR myelography showed the cyst followed the thecalsac. Signal intensity of the cystic mass was the same as the cerebrospinal fluid. In the prone position,laminectomy of the sacrum was carried out. The neck of the meningeal cyst was ligated with the help ofan aneurysmal needle. The patient's sensory disturbance disappeared postoperatively. As MRI becomesmore frequently used in Marfan syndrome, it is important to keep the presence of such an entity in mind.MR myelography made it easy to diagnose the meningeal cyst.