雑誌文献を検索します。書籍を検索する際には「書籍検索」を選択してください。

検索

書誌情報 詳細検索 by 医中誌

Japanese

A Case of Carney Complex Complicated with Pituitary Adenoma and Rathke Cleft Cyst Yuuta KAMOSHIMA 1 , Yutaka SAWAMURA 1 , Yoshinobu IWASAKI 1 , Kenji FUJIEDA 2 , Hiroyuki TAKAHASHI 3 1Department of Neurosurgery, Hokkaido University Graduate School of Medicine 2Department of Pediatrics, Asahikawa Medical College 3Department of Dermatology, Sapporo-Kousei General Hospital Keyword: acromegaly , Carney complex , pituitary adenoma , Rathke cleft cyst pp.535-539
Published Date 2008/6/10
DOI https://doi.org/10.11477/mf.1436100752
  • Abstract
  • Look Inside
  • Reference

 Carney complex is a rare autosomal-dominant, familial tumor syndrome first described in the mid 80's. This syndrome is multiple neoplasia syndrome featuring cardiac, endocrine, cutaneous, and neural tumor, in addition to a variety of pigmented lesions of the skin and mucosa. We report the case of a 12-year-old female patient with Carney complex who manifested a high value of serum growth hormone (s-GH), cutaneous angiomyxomas and labial pigmented lesions. Magnetic resonance imaging (MRI) revealed a cystic pituitary tumor. We carried out removal of the pituitary tumor via the transsphenoidal approach. In addition to the pituitary adenoma, pathological examination revealed the presence of a Rathke cleft cyst. So far, approximately 500 cases of this disorder have been described, but there have been no cases similar to our case described here. Therefore, the present case seems to be the first case of Carney Complex complicated with pituitary adenoma and Rathke cleft cyst.


Copyright © 2008, Igaku-Shoin Ltd. All rights reserved.

基本情報

電子版ISSN 1882-1251 印刷版ISSN 0301-2603 医学書院

関連文献

もっと見る

文献を共有