Differential Diagnosis of Idiopathic Cerebellar Ataxia Satoshi Kuwabara 1 1Department of Neurology, Graduate School of Medicine, Chiba University Keyword: 特発性小脳失調症 , 二次性小脳性運動失調症 , 多系統萎縮症 , 脊髄小脳失調症 , 自己免疫性小脳性運動失調症 , idiopathic cerebellar ataxia , secondary cerebellar ataxia , multiple system atrophy , spinocerebellar ataxia , immune-mediated cerebellar ataxia pp.969-972
Published Date 2020/9/1
DOI https://doi.org/10.11477/mf.1416201630
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Cortical cerebellar atrophy has been defined as a sporadic degenerative cerebellar disorder other than multiple system atrophy, whereas the term “idiopathic cerebellar ataxia (IDCA)” has been recently proposed by a Japanese expert group. There is no diagnostic biomarker for IDCA; therefore, the diagnosis largely depends on exclusion of other cerebellar diseases, such as multiple system atrophy and hereditary spinocerebellar ataxia. Other important differential diagnoses include immune-mediated cerebellar ataxia, such as Hashimoto's encephalopathy, gluten ataxia, anti-glutamic acid decarboxylase-positive cerebellar ataxia, alcoholic cerebellar degeneration, and drug-induced ataxia. Secondary cerebellar disorders are treatable and should be recognized and screened.

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