円錐角膜を合併したWagner様網膜硝子体変性症の1例

Wagner-like vitreoretinal degeneration with ker-atoconus

　症例は両眼霧視を主訴とする30歳女性で，両眼の高度近視，後嚢下白内障，網膜硝子体変性，円錐角膜を認めた。視力はハードコンタクトレンズ矯正下で右0.5左0.4,Wagner病様の網膜硝子体変性（液化硝子体，スイスチーズ様の孔，厚い硝子体膜，網膜硝子体索，網膜色素沈着，白鞘化した血管など）をみたが，網膜裂孔，網膜剥離，全身症状などはなく，色覚，視野，ERGはほぼ正常，3代にわたり家系内に異常者はなかった。今まで報告のない円錐角膜を合併したWagner様網膜硝子体変性症と考えられる。

A 30-year-old woman with Wagner-like vitreor-etinal degeneration was studied. The main symp-tom was a decreased vision of both eyes probably due to complicated cataract. Right visual acuity was 0.5 with HCL, and left was 0.4 with HCL. She didn't complain night blindness. Her ocular signs included high myopia, cataract (posterior subcap-sular opacity), vitreoretinal degeneration and ker-atoconus. The vitreoretinal change was likeWagner's disease (liquefaction of vitreous, opti-cally empty vitreous cavity, vitreous fibers or membranes, retinal pigment spots, narrow and sheathed retinal vessels, etc) without retinal break or retinal detachment. Color vision, visual field and the ERG were almost within normal range. She was not associated with systemic abnormalities, and didn't have any family history within 3 generations. This case was thought to be Wagner-like vitreo-retinal degeneration with keratoconus.