近位筋筋力低下と女性化乳房を呈した54歳男性

A 54-year-old Man with Progressive Proximal Muscle Atrophy and Gynecomastia

症例呈示

　症例　T．K，54歳，男性（93-84866）

　主訴　筋力低下，筋萎縮。

We report a 54-year-old man with progressive proximal muscle atrophy and gynecomastia. The patient had an insidious onset of weakness in his lower extremities at age 14, in that he noted a difficulty in standing up from a chair. Soon after he noted some difficulty in climbing up stairs. At age 35, he noted weakness in his arms; his weakness slowly progressed in that he became unable to walk or stand alone before 40 years of age. He also noted gynecomastia at that age. He was admitted to our hospital for the work up on September 16, 1993, when he was 54-year-old.