全身筋萎縮と，末期に至り眼球運動障害を呈した54歳男性

A 54-year-old Man with Generalized Muscle Atrophy and Oculomotor Paresis

症例呈示

　症例　Y．A．54歳，男性。

　主訴　全身筋力低下，筋萎縮。

We report a 54-year-old man with progressive generalized muscle atrophy and ophthalmoparesis in the terminal stage. He was well until 44 years of age (1982) when he noted weakness in his right hand and muscle atrophy ; in May of 1985, he noted weakness in his left hand and in both legs. His weakness had become progressively worse, and he became unable to walk in November of 1985. He noted dysarthria one month later, and dysphagia in March of 1986.