BRAIN and NERVE Shinkei Kenkyu no Shinpo Volume 68, Issue 2 (February 2016)

Clinical Importance of Central Nervous System Dysfunction in Myopathy Tsuyoshi Matsumura 1 1Department of Neurology, National Hospital Organization Toneyama National Hospital Keyword: 筋ジストロフィー , 集学的医療 , 中枢神経障害 , QOL , 患者の評価による治療効果 , muscular dystrophy , multidisciplinary treatment , central nervous system disturbance , quality of life , patient-reported outcome pp.109-118
Published Date 2016/2/1
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Multidisciplinary treatments including mechanical ventilation and cardioprotective therapy have improved life expectancy in many neuromuscular disorders such as Duchenne muscular dystrophy. For these patients, central nervous system disturbances such as intellectual and/or developmental disability can hinder social activities and communications. In myotonic dystrophy, the personality and/or cognitive dysfunction affects medical consultation behavior and decreases the efficacy of medical treatments. Understanding central nervous system disturbances in myopathies and providing care keeping in mind the patient burden are critical for improving prognosis and quality of life.

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BRAIN and NERVE-神経研究の進歩
68巻2号 (2016年2月)
電子版ISSN 1344-8129 印刷版ISSN 1881-6096 医学書院