水晶体，硝子体石灰沈着を伴つた相称性基底核石灰沈着症の1例

A CASE OF CALCIFICATION OF BILATERAI BASAL GANGLIA WITH CALCIFICATION OF LENS AND VITREOUS

I．はじめに

　1935年Fritzeが頭蓋レ線像て脳基底核部に相当する左右相性石灰沈着陰影を認め報告してから，本症の報告よ次第にその数を増し，今日では77例の報告をみるにいたつた^2）。しかしながらこの報告は欧米のみにがぎられ，わが国においては今日までのところまだ記載がなく綜説をみるのみである^1）。ここに報告する症例はわが国最初の報告と考えられる。

A case of calcification of symmetrical bilateral basal ganglia was reported. This is the first reported case in Japan.

A 39 years old man visited to the clinic because of repitition of maniac and depressive condition, and difficuity of speech. He was slightly short stature.

Radiograms of the skull revealed bilateral sym-metrical calcification which was suggested by PEG situated in the globus pallidus. Besides, there was calcification of the lens and vitrous of the left eye. There were cystic changes in bones of hands and foot, and distal portion of fibula an tibia.

In this case, no evidence of clinical and biochemical change was found, and other members of his families were free of intracranial calcification.