経過中に胆嚢癌を合併した先天性胆道拡張症の1例

Carcinoma of the Biliary Tract Associated with Congenital Bile Duct Dilatation

要旨　約3年間の経過中に胆嚢癌を合併し，その後約1年3か月で死亡した先天性胆道拡張症の1例を報告した．また，先天性胆道拡張症の自験16例についても，その概要を検討した．先天性胆道拡張症では50歳以上の例に胆道癌の合併が高率にみられるが，若年者にもまれではない．先天性胆道拡張症では胆嚢・胆管切除手術が治療の原則であり，術前に癌合併の有無をPTCDによる胆道二重造影を行って診断すべきである．

　Sixteen cases of patients with congenital bile duct dilatation were followed-up for a maximum period of 51 months. In six patients biliary carcinoma had developed. In four patients carcinoma was resected. The youngest patients was 17 year-old. Care must be taken in congenital bile duct dilatation since biliary carcinoma is frequently associated with it. Ultrasonography, transhepatic cholangiography with drain age followed by double contrast study of the biliary tract was effective for early diagnosis.