多発性囊胞腎患者にStanford B型急性大動脈解離・破裂を発症した1例

Thoracic Aortic Rupture of Stanford Type B Acute Aortic Dissection in a Patient with Polycystic Kidney Disease；Report of a Case

はじめに　多発性囊胞腎と急性大動脈解離の合併は，わが国において剖検例を含め20例程度であり，いまだ大動脈破裂例の報告はない．われわれは，多発性囊胞腎患者にStanford B型急性大動脈解離・破裂を発症し，部分弓部大動脈人工血管置換術により救命した症例を経験したので報告する．

We report a case of a 48-year-old man with polycystic kidney disease （PKD）, who was emergently transported to our institution by ambulance because of thoracic aortic rupture of Stanford type B acute aortic dissection. PKD is a congenital disease associated with hypertension （60％） and cerebrovascular disease （20％）. Few reports have described sudden death due to the rupture of an abdominal aortic aneurysm and acute aortic dissection. In this case, emergency hemi-arch replacement was performed successfully. His postoperative course was uneventful, and he was discharged on the 15th postoperative day.